Successful treatment of heart failure in an adult patient with Prader-Willi syndrome.
نویسندگان
چکیده
Prader-Willi Syndrome (PWS) is a rare genetic disorder characterized by physical, psychological and physiological abnormalities. Obesity and related cardiovascular diseases are a common problem in adult patients with PWS. This report describes a case of adult PWS with heart failure associated with marked obesity and sleep-disordered breathing that was successfully treated with oxygen therapy, adaptive servoventilation, medications, diet therapy and rehabilitation.
منابع مشابه
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ورودعنوان ژورنال:
- Internal medicine
دوره 52 7 شماره
صفحات -
تاریخ انتشار 2013